Hearing disorders and biotinidase deficiency: an integrative literature review
Alterações auditivas e deficiência de biotinidase: revisão integrativa da literatura
Tamara Miranda de Azevedo; Elaine Alvarenga de Almeida Carvalho; Sirley Alves da Silva Carvalho; Ana Lúcia Pimenta Starling; Rodrigo Rezende Arantes; Valeska Letícia Gonçalves Rodrigues; Adriane da Silva Assis; Vinícius Soares Garcia; Patrícia Cotta Mancini
Abstract
Keywords
Resumo
Objetivo: revisar a literatura disponível sobre a relação entre alterações auditivas e deficiência da biotinidase.
Métodos: a busca foi realizada entre outubro de 2018 e agosto de 2021, nas bases de dados: ELSEVIER, MEDLINE, SciELO, LILACS. Utilizaram-se descritores em português, inglês e espanhol, além das ferramentas PRISMA para seleção dos artigos e STROBE para análise dos mesmos.
Revisão da Literatura: foram selecionados artigos publicados entre 1983 e 2020 que respondiam à pergunta norteadora da pesquisa. Foram incluídos estudos observacionais, estudos de série de casos e relatos de caso, e excluídos os artigos sem descrição dos métodos utilizados, realizados pelo mesmo autor e com a mesma amostra. A estratégia de busca inicial identificou 152 artigos. Após aplicados os critérios de inclusão e exclusão, 14 artigos foram incluídos na presente revisão.
Conclusão: a presença de biotina foi frequentemente associada à gênese das vias auditivas. Foi observada uma relação sugerida pela literatura entre deficiência da biotinidase e alterações auditivas.
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Referencias
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Submitted date:
02/02/2021
Accepted date:
11/10/2021
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